Data for Metabolite-phenotype link in X-linked Adrenoleukodystrophy (part II) (Study ST000742)

(Analysis AN001158)

Values for each metabolite have been scaled by dividing by the mean across all factors

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MetaboliteF1F2F3F4F5F6F7F8
16:0-18:0 PC (M+NA)+ 0.9808 1.0442 0.7801 1.3029 NA 0.3392 0.3974 NA
16:0 LYSO PC (M+NA)+ 0.8309 1.0071 0.9315 0.9048 1.2462 1.2062 1.3482 NA
1-METHYLXANTHINE (M+H)+ 0.5787 0.8757 1.3686 1.2051 NA 0.3408 NA NA
1-OLEOYL-RAC-GLYCEROL (M+H)+ 0.9685 1.3835 1.0753 0.5671 0.6519 0.9201 1.1905 NA
1-OLEOYL-RAC-GLYCEROL (M+H)+[-H2O] 1.2522 1.8468 0.8485 0.5970 0.5660 0.5236 0.7235 NA
1-OLEOYL-RAC-GLYCEROL (M+NA)+ 1.0609 1.3847 0.6336 0.5014 0.8729 1.5756 1.7401 NA
25-HYDROXYCHOLESTEROL (M+H)+[-H2O] 0.8585 0.7322 1.0023 1.5093 0.8405 1.2458 0.6757 NA
3-AMINOISOBUTANOATE (M+H)+[-H2O] 0.6659 0.9958 1.1451 1.1664 NA NA NA NA
3-METHYLHISTAMINE (M+H)+ 0.1158 0.3357 2.7982 1.5734 1.0101 2.1179 1.0713 NA
4-ACETAMIDOBUTANOATE (M+NA)+ 0.5905 1.0081 1.1032 1.2738 NA NA NA NA
5-AMINOPENTANOATE (M+H)+ 0.7892 1.1339 1.4795 1.5477 0.1860 0.2545 0.1371 NA
5-OXOPROLINE (M+H)+ 0.5854 1.2742 0.7837 1.2933 0.8479 1.0174 0.9143 NA
ACETAMINOPHEN (TN TYLENOL) (M+NA)+ 0.1065 1.2379 0.9750 1.1204 NA NA NA NA
ALPHA-LINOLENIC ACID (M+NA)+ 0.5551 0.9046 1.0824 0.9716 1.0355 1.7722 1.3735 NA
ASPARTATE (M+H)+ 2.0969 0.3121 0.1356 0.1214 1.1825 0.9615 1.1908 NA
ASPARTATE (M+NA)+ 0.9459 0.6920 0.3534 0.3489 1.4190 1.2040 1.3283 NA
AZELAIC ACID (M+H)+[-H2O] 0.6926 0.9797 1.6555 1.0611 0.5791 0.5486 1.1424 NA
BETA-ALANYL-N(PAI)-METHYL-L-HISTIDINE (M+H)+ 1.9210 1.3665 0.5260 0.5666 0.7263 0.7137 0.8040 NA
BETA-ALANYL-N(PAI)-METHYL-L-HISTIDINE (M+NA)+ 1.4507 1.4586 0.6599 0.8914 0.3165 0.3545 0.3324 NA
BILIVERDIN (M+H)+ NA 0.8525 1.9396 0.9964 0.1756 0.1745 0.2160 NA
BUTYRYLCARNITINE (*) (M+H)+ 0.0616 0.8957 2.8927 1.6331 0.0986 0.1228 0.1578 NA
CARNITINE (M+H)+ 0.4855 0.5730 1.4343 1.2233 1.0920 1.0392 1.5272 NA
CHOLINE M+ 1.3544 0.8357 1.0210 0.8765 0.8814 0.9854 1.0182 NA
CHOLINE PHOSPHATE (M+H)+ 1.7918 1.0928 0.6044 0.6730 0.8149 1.0332 0.7282 NA
CHOLINE PHOSPHATE (M+NA)+ 0.8544 1.4306 1.4014 1.2966 0.3445 0.3081 0.4552 NA
CITRULLINE (M+H)+ 0.9285 1.3934 1.0591 1.7692 0.0594 0.0275 0.0955 NA
CITRULLINE (M+NA)+ 1.6126 1.3370 0.5632 1.2993 0.3358 0.2519 0.1889 NA
CYSTATHIONINE (M+H)+ 1.6947 0.4324 0.3409 0.9876 NA NA NA NA
CYSTINE (M+H)+ 1.2335 0.6497 0.7480 1.3757 0.1341 NA NA NA
CYSTINE (M+NA)+ 0.2472 0.5093 0.5289 0.8849 1.8964 2.8848 2.0040 NA
CYTIDINE 5^-DIPHOSPHOCHOLINE (M+H)+ 0.4907 1.0132 1.3285 1.3737 0.9912 0.7589 0.6293 NA
CYTIDINE 5^-DIPHOSPHOCHOLINE (M+K)+ 0.7749 1.1355 0.8936 0.9867 1.1638 1.0500 1.3666 NA
EPIBRASSINOLIDE [ISTD] (M+NA)+ 0.8188 0.9339 1.1567 1.0407 1.0292 1.0210 1.0914 NA
GAMMA-L-GLUTAMYL-L-CYSTEINE (M+H)+ 1.7925 0.9217 0.9935 0.9573 0.0951 0.0790 0.0561 NA
GAMMA-L-GLUTAMYL-L-CYSTEINE (M+H)+[-H2O] 0.5758 0.8850 1.6263 1.1161 0.4958 0.4550 NA NA
GLUCOSE (M+NA)+ 0.9196 1.4511 1.2634 1.3221 0.2782 0.2349 0.2363 NA
GLUTAMATE (M+H)+[-H2O] 0.9429 1.0774 0.9701 0.6768 1.3378 1.3245 1.3200 NA
GLUTATHIONE OXIDIZED (M+H)+ 0.3747 0.3057 0.4588 0.5080 3.4008 2.4687 2.5593 NA
GUANINE (M+H)+ 1.1173 0.4696 1.4449 1.3365 0.1295 0.1296 0.0778 NA
GUANOSINE 5^-PHOSPHATE (M+H)+ 0.7529 0.8870 0.4438 0.4465 1.9671 1.3808 1.7490 NA
GUANOSINE (M+H)+ 1.0278 0.7421 0.8367 0.8119 1.3518 1.7974 1.2786 NA
HEXANOYLCARNITINE (*) M+ 0.0371 0.7663 2.0883 1.8307 0.0432 0.0523 0.0670 NA
HISTAMINE (M+H)+ 0.0982 0.2549 2.5480 1.5727 0.0496 0.1588 0.1643 NA
HYPOXANTHINE (M+H)+ 1.3528 0.9758 1.3497 1.1661 0.2750 0.3907 0.3698 NA
INOSINE (M+NA)+ 0.9808 0.7790 0.4680 1.1481 1.6430 1.6385 0.7709 NA
ISOLEUCINE (M+H)+ 0.9024 1.0991 1.4195 1.3414 0.2987 0.4622 0.3726 NA
L-[15N]ANTHRANILIC ACID [ISTD] (M+H)+ 0.9144 0.8058 0.8260 1.1615 1.0708 1.1213 1.3452 NA
L-ARGININE (M+H)+ 0.6322 1.1162 1.7055 1.4517 0.1999 0.2034 0.1512 NA
LEUCINE (M+NA)+ 0.5827 1.0182 1.0940 1.3544 NA 0.0585 NA NA
L-TRYPTOPHAN-15N2 [ISTD] (M+H)+ 0.8383 0.9439 1.1237 1.0479 1.0169 1.0245 1.0758 NA
LYSINE (M+H)+ 0.8101 1.0134 1.3758 1.3427 0.4960 0.6181 0.3906 NA
METHIONINE (M+H)+ 0.8415 1.0266 1.3768 1.4777 0.3600 0.4196 0.3415 NA
N-ACETYL-DL-METHIONINE (M+H)+ 0.9227 1.4142 1.2574 1.4193 0.1463 0.1449 0.1501 NA
N-ACETYL-DL-METHIONINE (M+NA)+ 0.9089 1.4637 1.2707 1.4058 0.1211 0.1264 0.1242 NA
N-ACETYL-DL-SERINE (M+H)+[-H2O] 0.6660 0.7925 0.4978 1.7931 0.5365 1.5054 1.3073 NA
N-ACETYL-L-ASPARTIC ACID (M+H)+ 1.5469 0.5070 0.2998 0.1600 2.0159 2.3172 2.1814 NA
N-ACETYL-L-ASPARTIC ACID (M+NA)+ 1.7180 0.4949 0.3863 0.1928 1.9701 1.8825 1.8258 NA
NICOTINAMIDE (M+H)+ 0.6174 0.6207 0.9345 0.8315 1.7472 1.9391 1.7280 NA
N-METHYL-D-ASPARTIC ACID (M+H)+ 1.7266 0.7600 0.5127 0.4853 1.7075 1.2432 1.3529 NA
N-METHYL-D-ASPARTIC ACID (M+NA)+ 1.4200 0.9760 1.0653 0.8343 1.0063 0.6876 0.7370 NA
O-PHOSPHOSERINE (M+NA)+ 1.6330 0.9673 0.7653 0.5771 0.9811 0.6878 0.8373 NA
P-ACETAMIDOPHENYL BETA-D-GLUCURONIDE (M+H)+ NA 0.7611 1.0065 1.2337 NA NA NA NA
PANTOTHENATE (M+H)+ 0.8556 0.6615 1.0878 0.8381 1.2442 1.5654 1.6273 NA
PHENYLALANINE (M+H)+ 1.5026 0.6911 0.4569 0.8096 1.9152 0.7644 1.5259 NA
RAC-GLYCEROL 1-MYRISTATE (M+NA)+ 0.8880 2.4623 1.0103 0.8369 0.3832 0.5131 0.4153 NA
RIBOFLAVIN (M+H)+ 0.5629 0.8043 1.9392 1.2811 0.4630 0.6219 0.5243 NA
S-ADENOSYL-L-HOMOCYSTEINE (M+H)+ 0.7072 0.9834 1.6292 1.2163 0.5020 0.8177 0.5670 NA
SARCOSINE (M+H)+ 1.1686 0.7340 0.7952 0.6971 1.5908 1.4388 1.5161 NA
SN-GLYCERO-3-PHOSPHOCHOLINE (M+H)+ 0.4243 0.9875 1.6130 1.7141 0.2889 0.3452 0.3700 NA
SPERMIDINE (M+H)+ 2.6304 0.9946 0.4295 0.3733 0.8922 0.4774 0.4422 NA
SUCROSE (M+NA)+ NA 2.4354 0.3890 0.4504 NA NA NA NA
TAURINE (M+H)+ 0.7880 1.1674 0.7370 1.1699 1.1620 1.1417 0.9604 NA
TAURINE (M+NA)+ 0.6211 0.6827 0.7545 0.7120 1.9426 2.0569 1.8840 NA
TETRADECENOYLCARNITINE (*) M+ 1.6783 0.9706 0.5769 0.8046 0.5531 0.5637 0.7422 NA
TRYPTOPHAN (M+NA)+ 0.7545 0.9211 1.6851 1.3495 0.4242 0.4330 0.3993 NA
TYROSINE (M+H)+ 0.7597 0.9763 1.5033 1.5748 0.2260 0.3955 0.2636 NA
URIDINE (M+H)+ 0.7204 0.4159 0.7500 0.5237 1.4437 1.3406 1.8248 NA
VALINE (M+H)+ 0.9655 0.9995 1.3160 1.5168 0.2747 0.3689 0.2555 NA
XANTHINE (M+H)+ 1.1181 0.8775 1.2337 1.0356 0.7237 1.0718 0.6405 NA
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Factors:

F1Species:Homo sapiens | TYPE:Healthy control
F2Species:Homo sapiens | TYPE:NLA
F3Species:Homo sapiens | TYPE:PL
F4Species:Homo sapiens | TYPE:PLS
F5Species:Mus musculus | TYPE:ALD-KO
F6Species:Mus musculus | TYPE:KO-M
F7Species:Mus musculus | TYPE:WT
F8Species:- | TYPE:-
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