| Pathway name (# of metabolites detected in study) | Reactome pathway |
|---|---|
| Biotin transport and metabolism | REACT_11153 |
| Defective HLCS causes multiple carboxylase deficiency | REACT_169312 |
| Gluconeogenesis | REACT_1520 |
| Transport of vitamins, nucleosides, and related molecules | REACT_22285 |